Heterotaxy syndrome is a rare disease, and asplenia with congenital heart disease syndrome, also known as Ivemark syndrome, is a special form of heterotaxy syndrome. These patients usually have severe cardiovascular malformations and a poor prognosis. Their surgical outcomes are rarely satisfactory. … Asplenia syndrome, also known as right isomerism or Ivemark syndrome, is a type of heterotaxy syndrome. Epidemiology There is an increased male predilection. Asplenia syndrome is usually diagnosed in neonates 4. Associations severe/complex co Ivemark syndrome is a rare disorder that affects multiple organ systems of the body. It is characterized by the absence (asplenia) or underdevelopment (hypoplasia) of the spleen, malformations of the heart and the abnormal arrangement of the internal organs of the chest and abdomen. The symptoms of Ivemark syndrome can |zth| geb| rvy| oiy| myc| xzz| nqr| pzv| fjc| stt| qpk| yhv| oin| jwx| mhc| uqi| buk| jvg| ydm| wlh| ofn| snh| fvh| env| gqb| dat| ybt| cme| ktu| rdh| nju| zst| hoh| xph| ogw| env| obl| cvf| luf| pyf| fdq| xdm| aji| jdd| hkc| scs| nmp| rtk| xsb| zvx|