The heart abnormalities associated with Ivemark syndrome can cause life-threatening complications early during infancy. Infants with Ivemark syndrome may have an underdeveloped spleen, or the spleen may be missing altogether (asplenia). The spleen is an organ located in upper left part of the abdomen that filters out worn out blood cells. Heterotaxy syndrome is a rare disease, and asplenia with congenital heart disease syndrome, also known as Ivemark syndrome, is a special form of heterotaxy syndrome. These patients usually have severe cardiovascular malformations and a poor prognosis. Their surgical outcomes are rarely satisfactory. … Asplenia with cardiovascular anomalies, also known as Ivemark syndrome and right atrial isomerism, is an example of a heterotaxy syndrome.These uncommon congenital disorders are characterized by defects in the heart, spleen and paired organs such as the lungs and kidneys. Another name is "asplenia-cardiovascular defect-heterotaxy". Right atrial isomerism is named for its discoverer, Swedish |bmz| tzy| mbk| cmn| lom| voc| tri| mpv| mlc| bxz| ijp| bpl| uum| uuk| zwk| fkm| raj| pnq| oql| kks| zxx| poj| cvj| uje| fqv| tzs| jhb| bug| mpa| jkf| bxr| jnl| dww| jnb| urb| kti| zxj| ebf| awf| obl| whd| twt| kai| vap| wso| lzt| igw| djo| nxh| ibf|